Adult polycystic kidney disease (ADPKD) is an autosomal dominant condition that can be associated with several extrarenal manifestations including hepatic and pancreatic cysts, cardiac valve abnormalities, intracranial aneurysms, diverticulosis, and abdominal wall hernias. Pulmonary manifestations of ADPKD are scarcely described in literature. Only a couple of retrospective reports have described increased prevalence of radiographic bronchiectasis in patients with ADPKD. In this paper, we describe a young man with bronchiectasis as the sole presentation who was incidentally discovered to have ADPKD. A point of strength in this report is that other causes of bronchiectasis have been excluded by detailed history and extensive laboratory investigations.
Key-words:
Polycystic kidneys - Bronchiectasis - Autosomal dominant
