Primitive neuroectodermal tumor of the kidney: A rare case report

ABSTRACT

Renal primitive neuroectodermal tumor (PNET) is a rare primary renal neoplasm. Morphologically, it may mimic small blue round-cell tumor. Hence, histopathology in conjunction with immunohistochemistry plays a significant role in correctly diagnosing this malignancy. We report a case of PNET of kidney in a 30-year-old female with an extension to inferior vena cava, who succumbed following an aggressive course of illness.

Keywords

Histopathology - immunohistochemistry - primitive neuroectodermal tumor - renal - small-round-cell tumor

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