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CC BY-NC-ND 4.0 · Asian J Neurosurg 2020; 15(04): 1011-1015
DOI: 10.4103/ajns.AJNS_290_20
Case Report

Management of metastatic spine and hip alveolar soft part sarcoma: Case report and review of literature

Munjal Shah
Department of Spine Surgery, Lilavati Hospital and Research Centre, Mumbai, Maharashtra
,
Akshay Gadia
Department of Spine Surgery, Lilavati Hospital and Research Centre, Mumbai, Maharashtra
,
Abhay Nene
Department of Spine Surgery, Lilavati Hospital and Research Centre, Mumbai, Maharashtra
,
Priyank Patel
Department of Spine Surgery, Lilavati Hospital and Research Centre, Mumbai, Maharashtra
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Alveolar soft part sarcoma (ASPS) is a rare soft tissue tumor. Primary or metastatic involvement of the spine is unusual in ASPS. In most case, it is refractory to chemotherapy and radiation. Surgical resection is the most effective intervention. We report the case of a 38-year-old female having ASPS along with metastatic spine and hip involvement treated surgically as a single-stage operation, which is the first of its kind approach to our knowledge. We present the case of a 38-year-old female with simultaneous L4 pathological fracture with symptomatic lumbar canal stenosis without focal neurology and pathological fracture of neck of femur of left hip, secondary to metastatic ASPS. Since both conditions were contributing equally to her disability and demanded early intervention, they were treated simultaneously with intralesional excision of the tumor and posterior stabilization of the spine and left hip proximal femur resection and replaced it with proximal femur endoprosthesis as a single-stage operation. Postoperatively, she had significant relief of radiculopathy and left hip pain. She was mobilized out of bed on the postoperative day 1 and was discharged from hospital on the postoperative day 6. She was given chemotherapy drug sunitib postoperative. At her last follow-up, 20 months' postoperative, she was asymptomatic and was independent in terms of activities of daily living. Metastatic ASPS of the spine and hip is a rare clinical entity. Simultaneous surgical treatment of the spine and hip pathology is technically demanding. If the conditions demands, as in our case, both of them can be managed safely in a single-stage with good midterm outcome.

Key-words:

Alveolar soft part sarcoma - hip - metastasis - spine - surgery

Financial support and sponsorship

Nil.




Publication History

Received: 12 June 2020

Accepted: 24 September 2020

Article published online:
16 August 2022

© 2020. Asian Congress of Neurological Surgeons. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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