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CC BY-NC-ND 4.0 · Asian J Neurosurg 2021; 16(04): 846-849
DOI: 10.4103/ajns.AJNS_328_20
Case Report

Purely suprasellar (Hypothalamic) atypical teratoid rhabdoid tumor presenting with diabetes insipidus and panhypopituitarism in an adult male: A case report and review of literature

Ahmed Shaaban
1   Department of Neurosurgery, Hamad Medical Corporation, Doha
,
Amro Al Hajali
1   Department of Neurosurgery, Hamad Medical Corporation, Doha
,
Orwa Elaiwy
2   Department of Pathology, Hamad Medical Corporation, Doha
,
Ahmed El Sotouhy
3   Department of Radiology, Hamad Medical Corporation
4   Departments of Neurosurgery, Radiology and Pathology, Weill Cornell Medical College, Doha
,
Issam Al-Bozom
2   Department of Pathology, Hamad Medical Corporation, Doha
4   Departments of Neurosurgery, Radiology and Pathology, Weill Cornell Medical College, Doha
,
Ali Ayyad
1   Department of Neurosurgery, Hamad Medical Corporation, Doha
4   Departments of Neurosurgery, Radiology and Pathology, Weill Cornell Medical College, Doha
5   Department of Neurosurgery, Saarland University Hospital, Homburg, Germany
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Atypical teratoid rhabdoid tumor (ATRT) is a rare primary malignant tumor of the central nervous system. Little knowledge is available about natural history, behavior, prognosis, and best management guidelines of such tumor. Its occurrence in adults is very rare and more predominant in females. Locations in adults are mainly cerebral hemispheres, but recently, more cases are reported in sellar/suprasellar cisterns. We are reporting a case of purely suprasellar ATRT of a middle aged male who presented initially with diabetes insipidus (DI).

Key-words:

Atypical teratoid rhabdoid tumor - diabetes insipidus - suprasellar

Financial support and sponsorship

Nil.




Publikationsverlauf

Eingereicht: 04. Juli 2020

Angenommen: 26. April 2021

Artikel online veröffentlicht:
16. August 2022

© 2021. Asian Congress of Neurological Surgeons. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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