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CC BY-NC-ND 4.0 · Asian J Neurosurg 2021; 16(03): 579-581
DOI: 10.4103/ajns.AJNS_499_20
Case Report

Dyke–davidoff–masson syndrome: A rare cause of acquired cerebral hemiatrophy

Deepak Bhol
Department of Pediatrics, All India Institute of Medical Sciences, Bhubaneswar, Odisha, India
,
Shyam Chandrasekar
Department of Pediatrics, All India Institute of Medical Sciences, Bhubaneswar, Odisha, India
,
Joseph John
Department of Pediatrics, All India Institute of Medical Sciences, Bhubaneswar, Odisha, India
,
Amit Satapathy
Department of Pediatrics, All India Institute of Medical Sciences, Bhubaneswar, Odisha, India
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Dyke–Davidoff–Masson syndrome is a rare disease of childhood which is clinically characterized by hemiparesis, refractory seizures, facial asymmetry, and mental retardation. The classical radiological findings are cerebral hemiatrophy, calvarial thickening, and hyperpneumatization of the frontal sinuses. Seizure refractory to medical management warrants surgical intervention with excellent outcome. Here, we are reporting two such cases who presented late and diagnosis was made on the basis of magnetic resonance imaging brain features. Both of our children responded to oral anticonvulsant and are on regular follow-up.

Key-words:

Calvarium thickening - cerebral hemiatrophy - Dyke–Davidoff–Masson syndrome - intellectual disability - seizures

Financial support and sponsorship

Nil.




Publikationsverlauf

Eingereicht: 20. November 2020

Angenommen: 13. Juni 2021

Artikel online veröffentlicht:
16. August 2022

© 2021. Asian Congress of Neurological Surgeons. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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