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CC BY-NC-ND 4.0 · Asian J Neurosurg 2021; 16(03): 598-602
DOI: 10.4103/ajns.AJNS_502_20
Case Report

Coincidence of intracranial myoepithelioma and adrenocortical carcinoma in a young man

Lai-Fung Li
Division of Neurosurgery, Department of Surgery, Li Ka Shing Faculty of Medicine The University of Hong Kong, Hong Kong
,
Ronnie Ho
1   Department of Pathology, Li Ka Shing Faculty of Medicine, The University of Hong Kong, Pok Fu Lam, Hong Kong
,
Anderson Tsang
Division of Neurosurgery, Department of Surgery, Li Ka Shing Faculty of Medicine The University of Hong Kong, Hong Kong
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Myoepithelial tumors are rare neoplasms that develop from myoepithelial cells in glandular structures and soft tissues. Primary intracranial myoepithelial neoplasms are even rarer with around ten cases reported. On the other hand, adrenocortical carcinoma (ACC) is also uncommon with an annual incidence of 0.7–2 per million and carries a poor prognosis. It is known to have an association with certain familial cancer syndromes. Even in sporadic cases, a significant portion of them had other malignancies before and after diagnosis of ACC. We reported a 34-year-old gentleman who was diagnosed to have ACC without known familial cancer syndrome. After that, he was also found to have right occipital myoepithelioma that was confirmed by excisional biopsy. There was no known association between these two pathologies. This is the first report of coincidence of ACC and intracranial myoepithelioma.

Key-words:

Adrenocortical carcinoma - brain neoplasms - myoepithelioma

Financial support and sponsorship

Nil.




Publikationsverlauf

Eingereicht: 21. November 2020

Angenommen: 10. April 2021

Artikel online veröffentlicht:
16. August 2022

© 2021. Asian Congress of Neurological Surgeons. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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