Neurocutaneous melanosis with hydrocephalus and dandy-walker variant

Mohammad Sarwar; Laxminarayan Tripathy; Harsh Jain; Sunandan Basu; Ashvini Sengupta

doi:10.4103/ajns.AJNS_542_20

Asian Journal of Neurosurgery, Table of Contents

CC BY-NC-ND 4.0 · Asian J Neurosurg 2021; 16(04): 876-880
DOI: 10.4103/ajns.AJNS_542_20

Case Report

Neurocutaneous melanosis with hydrocephalus and dandy-walker variant

Mohammad Sarwar

Department of Neurosurgery, Medica Institute of Neurological Diseases, Medica Superspecialty Hospital, Kolkata, West Bengal

,

Laxminarayan Tripathy

Department of Neurosurgery, Medica Institute of Neurological Diseases, Medica Superspecialty Hospital, Kolkata, West Bengal

,

Harsh Jain

Department of Neurosurgery, Medica Institute of Neurological Diseases, Medica Superspecialty Hospital, Kolkata, West Bengal

,

Sunandan Basu

Department of Neurosurgery, Medica Institute of Neurological Diseases, Medica Superspecialty Hospital, Kolkata, West Bengal

,

Ashvini Sengupta

¹Department of Laboratory Services, Medica Superspecialty Hospital, Kolkata, West Bengal

› Author Affiliations

Abstract

Neurocutaneous melanosis (NCM) is one of the rare, congenital, noninheritable phakomatoses characterized by the presence of large and/or multiple congenital melanocytic cutaneous nevi associated with intracranial leptomeningeal melanocytosis. NCM usually presents before 2 years of age. So far 302 cases have been reported in literature. We report a case of NCM presenting with obstructive hydrocephalus and Dandy-Walker Variant in a young adult.

Key-words:

Dandy-Walker variant - hydrocephalus - neurocutaneous melanosis - tuberculous meningitis

Full Text

References

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