A rare case of isolated intraventricular primary central nervous system lymphoma in an 85-year-old man

Primary CNS lymphoma (PCNSL) is rare malignant B cell lymphoid tumor of brain which predominantly occurs in supratentorial region in periventricular location. Majority of PCNSL are of DLBCL type and idiopathic in etiology. Here we are reporting a case of primary CNS lymphoma, DLBCL involving extremely uncommon intraventricular location. Central neurocytoma, subependymal giant cell astrocytoma, choroid plexus tumors and meningiomas are the common diagnosis at this site. Aim of reporting this case is to bring awareness of unusual intraventricular location of primary CNS lymphoma which should be kept in mind before considering gross total excision of lesion.

Key-words:

Primary CNS lymphoma - Intraventricular lymphoma - DLBCL

Financial support and sponsorship

Nil.

Publication History

Received: 22 December 2020

Accepted: 11 March 2021

Article published online:
16 August 2022

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