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CC BY-NC-ND 4.0 · Asian J Neurosurg 2021; 16(03): 447-451
DOI: 10.4103/ajns.AJNS_79_21
Review Article

Extra-axial cerebello-pontine angle medulloblastoma in an infant: A rare case report with review of literature

Santosh Prabhu
Department of Neurosurgery, Western India Institute of Neurosciences, Kolhapur, Maharashtra, India
,
Sidharth Agarwal
Department of Neurosurgery, Western India Institute of Neurosciences, Kolhapur, Maharashtra, India
,
Sujata Prabhu
Department of Neurosurgery, Western India Institute of Neurosciences, Kolhapur, Maharashtra, India
,
Akash Prabhu
Department of Neurosurgery, Western India Institute of Neurosciences, Kolhapur, Maharashtra, India
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Medulloblastoma is a fairly common neoplastic growth seen majorly in children, presenting as an intra-axial midline mass arising from the cerebellar vermis. However, its presentation as an extra-axial mass in the cerebellopontine angle (CPA) is extremely rare, such that, only 39 cases have been reported in the world literature till 2016. Only one case has ever been reported of an extra-axial CPA medulloblastoma in an infant; who was aged 1 year. We present a case report of an 8-month-old infant, with an extra-axial CPA medulloblastoma and discuss its management strategy.

Key-words:

Cerebellopontine angle - chemotherapy - medulloblastoma - radiotherapy

Financial support and sponsorship

Nil.




Publication History

Received: 22 February 2021

Accepted: 18 April 2021

Article published online:
16 August 2022

© 2021. Asian Congress of Neurological Surgeons. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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