CC BY-NC-ND 4.0 · Asian J Neurosurg 2019; 14(01): 289-291
DOI: 10.4103/ajns.AJNS_87_18
Case Report

Giant encephalocoele: A rare case report and review of literature

Vikas Naik
Department of Neurosurgery, Bangalore Medical College and Research Institute, PMSSY Super Speciality Hospital, Bengaluru, Karnataka
,
Vinay Marulasiddappa
1   Department of Anesthesiology, Bangalore Medical College and Research Institute, PMSSY Super Speciality Hospital, Bengaluru, Karnataka
,
Mandya Gowda Naveen
Department of Neurosurgery, Bangalore Medical College and Research Institute, PMSSY Super Speciality Hospital, Bengaluru, Karnataka
,
S Pai
Department of Neurosurgery, Bangalore Medical College and Research Institute, PMSSY Super Speciality Hospital, Bengaluru, Karnataka
,
Pratham Bysani
Department of Neurosurgery, Bangalore Medical College and Research Institute, PMSSY Super Speciality Hospital, Bengaluru, Karnataka
,
S Amreesh
Department of Neurosurgery, Bangalore Medical College and Research Institute, PMSSY Super Speciality Hospital, Bengaluru, Karnataka
› Author Affiliations

Giant encephalocoeles are rare entities with only one case series and few case reports reported in medical literature. Encephalocoeles, which reach a size larger than the head size, are be called Giant encephalocoeles. We report a case of a 6 month old child who had giant encephalocoele with delayed motor milestones in the form of inability to hold neck. Anesthetic implications include difficulty in securing air way due without undue pressure on the sac. She underwent VP shunt followed by excision of the encephalocele sac. Patient is doing well at 1 year of follow up. Preoperative neurological status and amount of brain tissue herniating into the sac are the most important factors determining the long term prognosis.

Financial support and sponsorship

Nil.




Publication History

Article published online:
09 September 2022

© 2019. Asian Congress of Neurological Surgeons. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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