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CC BY-NC-ND 4.0 · Ibnosina Journal of Medicine and Biomedical Sciences 2020; 12(01): 53-56
DOI: 10.4103/ijmbs.ijmbs_88_19
Case Report

Unusually long survival of an adult patient with atypical teratoid/rhabdoid tumor of the sellar region: A follow-up report

Mussa Almalki
1   Obesity, Endocrine and Metabolism Center, King Fahad Medical City, Kingdom of Saudi Arabia
2   King Fahad Medical City, College of Medicine, King Saud Bin Abdulaziz University for Health Science, Riyadh, Kingdom of Saudi Arabia
,
Abdullah Altwairgi
3   Oncology Center, King Fahad Medical City, Riyadh, Kingdom of Saudi Arabia
,
Yasser Orz
4   Department of Neurosurgery, National Neuroscience Institute, King Fahad Medical City, Riyadh, Kingdom of Saudi Arabia
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Atypical teratoid/rhabdoid tumor (AT/RT) is a rare and very aggressive central nervous system neoplasm that is most often seen in infants and young children. The prognosis remains poor, with a median survival time of <1 year. Here, we report a follow-up on a case of AT/RT that originated in the sellar and suprasellar region in a 42-year-old female patient with unusually long survival.

Key-words:

Adult - atypical teratoid/rhabdoid tumor - central nervous system neoplasm - prognosis

Financial support and sponsorship

Nil.




Publication History

Received: 21 January 2020

Accepted: 26 March 2020

Article published online:
07 July 2022

© 2020. The Libyan Authority of Scientific Research and Technologyand the Libyan Biotechnology Research Center. All rights reserved. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License,permitting copying and reproductionso long as the original work is given appropriate credit. Contents may not be used for commercial purposes, oradapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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