Extrarenal Extracranial Rhabdoid Tumor of the Pelvis in a Young Adult‑management of a Challenging Case

Bharti Devnani; Ahitagni Biswas; Sameer Bakhshi; Seema Kaushal; Tripti Nakra

doi:10.4103/ijmpo.ijmpo_108_17

Indian Journal of Medical and Paediatric Oncology, Inhaltsverzeichnis

CC BY-NC-ND 4.0 · Indian J Med Paediatr Oncol 2017; 38(03): 383-386
DOI: 10.4103/ijmpo.ijmpo_108_17

Case Report

Extrarenal Extracranial Rhabdoid Tumor of the Pelvis in a Young Adult‑management of a Challenging Case

Autor*innen

Bharti Devnani

Department of Radiotherapy and Oncology, All India Institute of Medical Sciences, New Delhi, India
Ahitagni Biswas

Department of Radiotherapy and Oncology, All India Institute of Medical Sciences, New Delhi, India
Sameer Bakhshi

Department of Medical Oncology, All India Institute of Medical Sciences, New Delhi, India
Seema Kaushal

Department of Pathology, All India Institute of Medical Sciences, New Delhi, India
Tripti Nakra

Department of Pathology, All India Institute of Medical Sciences, New Delhi, India

Abstract

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Abstract

Rhabdoid tumor commonly occurs in the kidney and has an aggressive clinical course with high mortality. Central nervous system is the most common extrarenal site. Extrarenal extracranial rhabdoid tumor (EERT) is rare. EERT usually presents in childhood, and presentation in adulthood is extremely rare. This tumor is often difficult to diagnose, and there is no established standard of care due to the paucity of cases. We herein report a case of extrarenal rhabdoid tumor of the pelvis in a young adult and discuss the presentation and possible treatment options of this rare tumor.

Keywords

Extracranial - extrarenal - INI-1 - pelvis - rhabdoid tumor

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Referenzen

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