Adrenocortical Carcinoma: A Rare Tumor in a 12-year-old Girl

Abstract

A 12-year-old girl presented with intra-abdominal mass and cushingoid features. On investigation, she was diagnosed as a case of functioning adrenocortical carcinoma. Two cycles of neoadjuvant chemotherapy followed by excision of mass with right nephrectomy was performed. On 6-month follow-up, recurrence and metastasis were identified which were managed with surgery and chemotherapy.

Keywords

Adrenocortical carcinoma - cushingoid - pediatric

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