CC BY-NC-ND 4.0 · Indian J Med Paediatr Oncol 2019; 40(S 01): S139-S141
DOI: 10.4103/ijmpo.ijmpo_232_17
Case Report

Primary Renal Leiomyosarcoma Arising from Renal Vein: A Case Report of Rare Entity with Review of Literature

Reetu Kundu
Departments of Pathology, Government Medical College and Hospital, Chandigarh, India
,
Mahesh Chandra
Departments of Urology, Government Medical College and Hospital, Chandigarh, India
,
Rajpal Singh Punia
Departments of Pathology, Government Medical College and Hospital, Chandigarh, India
,
Purnima Aggarwal
Departments of Radiodiagnosis, Government Medical College and Hospital, Chandigarh, India
› Author Affiliations
Financial support and sponsorship Nil.

Abstract

Primary renal sarcomas are extremely rare neoplasms accounting for about 1% of all malignant renal neoplasms. Among all the sarcomas of kidney, leiomyosarcoma is the most common histotype. The histogenesis of these tumors is unclear, and presumably, they arise either from renal capsule or smooth muscle of renal vessels or renal pelvis. We report a case of a 65-year-old woman, who presented with intermittent abdominal pain for 1 year. The correct diagnosis was established only after the histopathological analysis of the resected specimen. The poor prognosis borne by these tumors mandates a thorough evaluation of all renal masses with unusual gross and histomorphology.



Publication History

Article published online:
24 May 2021

© 2019. Indian Society of Medical and Paediatric Oncology. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).

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