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CC BY-NC-ND 4.0 · Indian J Med Paediatr Oncol 2017; 38(02): 236-239
DOI: 10.4103/ijmpo.ijmpo_46_16
Case Report

Hepatic Amyloidosis: Something That Can camouflage and Deceive our Perception!

Anirudh V Nair
Department of Radiodiagnosis and Interventional Radiology, Kerala Institute of Medical Science and Research Centre, Trivandrum, Kerala, India
,
Manish Kumar Yadav
Department of Radiodiagnosis and Interventional Radiology, Kerala Institute of Medical Science and Research Centre, Trivandrum, Kerala, India
,
Madhavan N Unni
Department of Radiodiagnosis and Interventional Radiology, Kerala Institute of Medical Science and Research Centre, Trivandrum, Kerala, India
,
CM Simi
Department of Pathology, Kerala Institute of Medical Science and Research Centre, Trivandrum, Kerala, India
,
KA Biji
Department of Pathology, Kerala Institute of Medical Science and Research Centre, Trivandrum, Kerala, India
,
KS Manoj
Department of Radiodiagnosis and Interventional Radiology, Kerala Institute of Medical Science and Research Centre, Trivandrum, Kerala, India
,
Shabeer Ali
Department of Hepatobiliary, Pancreatic and Liver Transplant Surgery, Kerala Institute of Medical Science and Research Centre, Trivandrum, Kerala, India
,
Ajith K Nair
Department of Gastroenterology, Kerala Institute of Medical Science and Research Centre, Trivandrum, Kerala, India
› Author Affiliations Financial support and sponsorship Nil.
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Abstract

Amyloidosis is a multi-systemic diffusely infiltrating disease due to extracellular deposition of protein-mucopolysaccharide complexes. The type of protein deposited determines the subgroup of amyloid. Hepatic amyloidosis is a rare infiltrating disease affecting the hepatic parenchyma. A wide range of clinical presentation and atypical imaging findings delay the diagnosis of amyloidosis, while tissue biopsy demonstrating amyloid deposits is vital for a definitive diagnosis.

Keywords

B mode ultrasound - contrast CT - hepatic amyloidosis - infiltrating disease - primary secondary amyloidosis


Publication History

Article published online:
06 July 2021

© 2017. Indian Society of Medical and Paediatric Oncology. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/.)

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