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CC BY-NC-ND 4.0 · Indian J Med Paediatr Oncol 2018; 39(02): 237-240
DOI: 10.4103/ijmpo.ijmpo_55_17
Practitioner Section

A Rare Nonhepatocytic Primary Liver Neoplasm with an Unusual Presentation: Ossifying Malignant Mixed Epithelial and Stromal Tumor

Albina Venus
Department of Pathology, Kovai Medical Center and Hospital, Coimbatore, Tamil Nadu, India
,
Sangita Sharma Mehta
Department of Pathology, Kovai Medical Center and Hospital, Coimbatore, Tamil Nadu, India
,
Sumathi Natarajan
Department of Radiology, Kovai Medical Center and Hospital, Coimbatore, Tamil Nadu, India
› Author Affiliations Financial support and sponsorship Nil.
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Abstract

We present a case of a rare liver neoplasm – Ossifyimg malignant mixed epithelial and stromal tumor. This entity has well-delineated morphological and immunohistochemical features, and so can be easily diagnosed, even with core biopsy tissue. Our patient was a middle-aged male, which is unheard of in the literature of this disease. He had a bad recurrence of the disease after surgical removal of the tumor, unlike the previously reported cases with the same diagnosis, where the patients lived for almost a decade after surgery without recurrence. This neoplasticdisease can thus take a destructive course, and a change in treatment methods such as neoadjuvant or adjuvant chemotherapy should be thought of, to make it more beneficial and effective.

Keywords

Adenocarcinomatous - mixed - nonhepatocytic - ossifying - primary - sarcomatous


Publication History

Article published online:
23 June 2021

© 2018. Indian Society of Medical and Paediatric Oncology. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/.)

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