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CC BY-NC-ND 4.0 · Indian J Radiol Imaging 2017; 27(04): 432-435
DOI: 10.4103/ijri.IJRI_389_16
Paediatric

Emergent presentation of Langerhans cell histiocytosis in a pediatric patient: Acute cerebellar involvement causing obstructive hydrocephalus requiring posterior fossa decompression

Dhanashree A Rajderkar
Department of Radiology, University of Florida, Gainesville, Florida, USA
,
Mrunal L Shah
Department of Radiology, University of Florida, Gainesville, Florida, USA
,
Jehan L Shah
Department of Radiology, University of Florida, Gainesville, Florida, USA
› Author Affiliations Financial support and sponsorship Nil.
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Abstract

Langerhans cell histiocytosis (LCH) is a disorder of the monocyte-macrophage system that can be unifocal or systemic. Here, we present a pediatric case who initially presented with osseous LCH but again presented 6 years later emergently with cerebellar symptoms, cerebellar mass and obstructive hydrocephalus. Patient underwent biopsy of the cerebellum which was path proven intracranial LCH.

Keywords

Emergent decompression - intracranial Langerhans cell histiocytosis - obstructive hydrocephalus


Publication History

Article published online:
27 July 2021

© 2017. Indian Radiological Association. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).

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