Abstract
Rhabdomyosarcoma (RMS) is a malignant mesenchymal tumor arising from the embryonal
muscle cells (rhabdomyoblasts), and is the most common soft tissue sarcoma in children
and young adults accounting for 4–6% of all malignancies in this age group. Though
rare overall, embryonal rhabdomyosarcoma is the most common malignancy arising in
the pediatric female genitourinary tract with sarcoma botryoides being the most common
variant of the tumor. In young and adolescent individuals, the cervix and uterus are
affected; whereas in infants, vaginal lesions are more common. Imaging plays a crucial
role not only in the initial diagnosis but also in long-term follow-up of genital
RMS. We describe a rare case of embryonal rhabdomyosarcoma of the vagina occurring
in a 23-year-old female who presented with abnormal vaginal bleeding ever since she
was a child.
Keywords
Embryonal rhabdomyosarcoma - sarcoma botryoides - vaginal tumor
