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CC BY 4.0 · Brazilian Journal of Oncology 2021; 17: e-20210031
DOI: 10.5935/2526-8732.20210031
Case Report
Oncological Surgery

Solid pseudopapillary tumor associated with agenesis of the dorsal pancreas: a case report

Tumor sólido pseudopapilar associado à agenesia dorsal do pâncreas: relato de caso
Daniel Paulino Santana
1   Hospital Integrado do Câncer - Rede Mater Dei de Saúde, Surgical Oncology - Belo Horizonte - MG - Brazil
,
Diogo Viana Abreu
2   Fundação Benjamim Guimarães - Hospital da Baleia, General Surgery - Belo Horizonte - MG - Brazil
,
Edmilson Celso Santos
1   Hospital Integrado do Câncer - Rede Mater Dei de Saúde, Surgical Oncology - Belo Horizonte - MG - Brazil
,
Bruno de Lima Rodrigues
1   Hospital Integrado do Câncer - Rede Mater Dei de Saúde, Surgical Oncology - Belo Horizonte - MG - Brazil
,
Anna Carolina D'Ascenção Maia
3   Hospital Integrado do Câncer - Rede Mater Dei de Saúde, Clinical Oncology - Belo Horizonte - MG - Brazil
,
Marcos Campos Wanderley Reis
1   Hospital Integrado do Câncer - Rede Mater Dei de Saúde, Surgical Oncology - Belo Horizonte - MG - Brazil
› Author Affiliations Financial support: None to declare.
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ABSTRACT

Solid pseudopapillary tumors (SPTs) of the pancreas are rare tumors with low potential for malignancy, uncertain lineage, and favorable prognosis in most cases. The SPT has an excellent prognosis, and the standard treatment is surgical resection. The agenesis of the dorsal pancreas (ADP) is an extremely rare type of congenital pancreatic malformation and is characterized by partial or total loss of the body and tail of the gland. Its association with SPT has been reported only in two studies. We report a case of SPT associated with total ADP. A 36-year-old woman was diagnosed with a complex mass on pancreatic head topography, measuring 7.8×5.5cm, associated with complete agenesis of the body and tail of the pancreas. She underwent gastropancreatoduodenectomy with a successful postoperative outcome. The anatomopathological examination suggested an SPT and it was confirmed by immunohistochemistry.

RESUMO

Os tumores sólidos pseudopapilares (TSPs) do pâncreas são tumores raros com baixo potencial de malignidade, linhagem incerta e prognóstico favorável na maioria dos casos. O SPT tem excelente prognóstico e o tratamento padrão é a ressecção cirúrgica. A agenesia dorsal do pâncreas (ADP) é um tipo extremamente raro de malformação congênita do pâncreas e é caracterizada pela perda parcial ou total do corpo e cauda da glândula. Sua associação com TSP foi relatada apenas em dois estudos. Relatamos um caso de TSP associado à ADP total. Uma mulher de 36 anos foi diagnosticada com uma massa complexa na topografia da cabeça do pâncreas, medindo 7,8×5,5cm, associada à agenesia completa do corpo e cauda do pâncreas. Ela foi submetida à gastropancreatoduodenectomia com sucesso pós-operatório. O exame anatomopatológico sugeriu TSP e foi confirmado por imunohistoquímica.

Keywords:

Pancreatic neoplasms - Pancreatic cancer - Pancreatectomy - Pancreas - Agenesis.

Descritores:

Neoplasias pancreáticas - Câncer pancreático - Pancreatectomia - Pâncreas - Agenesia


Publication History

Received: 29 March 2021

Accepted: 05 August 2021

Article published online:
07 December 2021

© 2021. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution 4.0 International License, permitting copying and reproduction so long as the original work is given appropriate credit (https://creativecommons.org/licenses/by/4.0/)

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Bibliographical Record
Daniel Paulino Santana, Diogo Viana Abreu, Edmilson Celso Santos, Bruno de Lima Rodrigues, Anna Carolina D'Ascenção Maia, Marcos Campos Wanderley Reis. Solid pseudopapillary tumor associated with agenesis of the dorsal pancreas: a case report. Brazilian Journal of Oncology 2021; 17: e-20210031.
DOI: 10.5935/2526-8732.20210031
 

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