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DOI: 10.5935/2526-8732.20220343
Incidental finding of sex cord tumor with annular tubules in ovary associated with Peutz-Jeghers syndrome
Achado incidental de tumor do cordão sexual com túbulos anulares em ovário associado à síndrome de Peutz-Jeghers Financial support: None to declare.
ABSTRACT
Sex cord tumor with annular tubules (SCTAT) is a rare ovarian pathology. It is usually an incidental finding in asymptomatic patients. In about 30% of cases, this tumor is associated with the Peutz-Jeghers syndrome (PJS). This case report describes an incidental finding of SCTAT during an excisional surgery of a giant mucinous cystadenoma in the contralateral ovary. In addition to the finding of a rare tumor in association with a rare syndrome, a literature review on the diseases, their association, and management was performed.
RESUMO
O tumor do cordão sexual com túbulos anulares (TCSTA) é uma patologia ovariana rara. Geralmente é um achado incidental em pacientes assintomáticos. Em cerca de 30% dos casos, esse tumor está associado à síndrome de Peutz-Jeghers (SPJ). Este relato de caso descreve um achado incidental de TCSTA durante uma cirurgia excisional de um cistoadenoma mucinoso gigante no ovário contralateral. Além do achado de um tumor raro associado a uma síndrome rara, foi realizada uma revisão da literatura sobre as doenças, sua associação e manejo.
Keywords:
Peutz-Jeghers syndrome - Sex cord-gonadal stromal tumors - Ovarian sex cord-stromal tumours - Mucinous cystadenoma - Mucinous ovarian tumorsPalavras-chave:
Síndrome de Peutz-Jeghers - Tumores do estroma cordão-gonadal sexual - Tumores do cordão sexual ovariano - Cistadenoma mucinoso - Tumores mucinosos do ovárioPublication History
Received: 04 April 2022
Accepted: 18 May 2022
Article published online:
22 June 2022
© 2022. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution 4.0 International License, permitting copying and reproduction so long as the original work is given appropriate credit (https://creativecommons.org/licenses/by/4.0/)
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Nathalia Beck Corrêa, Laura Paggiarin Skonieski, Francisco Costa Beber Lemanski, Rafael Baldissera. Incidental finding of sex cord tumor with annular tubules in ovary associated with Peutz-Jeghers syndrome. Brazilian Journal of Oncology 2022; 18: e-20220343.
DOI: 10.5935/2526-8732.20220343
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