Aktuelle Bildgebungsstrategien bei genetisch bedingten Erkrankungen der Aorta

Julius Matthias Weinrich; Alexander Lenz; Evaldas Girdauskas; Gerhard Adam; Yskert von Kodolitsch; Peter Bannas

doi:10.1055/a-0986-9611

Gefäßmedizin Scan - Zeitschrift für Angiologie, Gefäßchirurgie, diagnostische und interventionelle Radiologie, Table of Contents

Gefäßmedizin Scan - Zeitschrift für Angiologie, Gefäßchirurgie, diagnostische und interventionelle Radiologie 2019; 06(03): 227-239
DOI: 10.1055/a-0986-9611

CME-Fortbildung

Aktuelle Bildgebungsstrategien bei genetisch bedingten Erkrankungen der Aorta

Julius Matthias Weinrich

,

Alexander Lenz

,

Evaldas Girdauskas

,

Gerhard Adam

,

Yskert von Kodolitsch

,

Peter Bannas

Subject Editor: Wissenschaftlich verantwortlich gemäß Zertifizierungsbestimmungen für diesen Beitrag ist Dr. Julius Matthias Weinrich, Hamburg.

Abstract

Genetische Aortenerkrankungen sind vielfältig und haben aufgrund hoher Morbiditäts- und Mortalitätsraten einen besonderen Stellenwert. Die radiologische Bildgebung ist essenziell in der Diagnosestellung, Verlaufskontrolle und Indikationsstellung zum prophylaktischen Aortenwurzelersatz. Im folgenden Artikel werden die häufigsten genetischen Aortenerkrankungen und die empfohlene Bildgebung mit Ausblick auf moderne Techniken vorgestellt.

Schlüsselwörter

Genetisch bedingtes Aortensyndrom - Loeys-Dietz-Syndrom - Ehlers-Danlos-Syndrom - Marfan-Syndrom - bildgebende Diagnostik

Full Text

References

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