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Klinische Neurophysiologie 2021; 52(02): 112-114
DOI: 10.1055/a-1272-9542
Der besondere Fall

Syndrom des zweiten Motoneuron mit „snake eyes“ der cervikalen Vorderhörner im MRT – gutartige Differenzialdiagnose der ALS

Lars Schönlau
Klinik für Neurologie, Universitätsklinikum Knappschaftskrankenhaus Bochum GmbH, Bochum
,
Helmut Buchner
Klinik für Neurologie, Universitätsklinikum Knappschaftskrankenhaus Bochum GmbH, Bochum
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Warum dieser Fall

Der Fall zeigt die Unterscheidung einer Läsion des zweiten Motorneurons von der peripherer Nerven. Die seltene Ursache der Motorneuronerkrankung ist eine Differenzialdiagnose der ALS.



Publication History

Article published online:
28 January 2021

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  • Literatur

  • 1 Lebouteux MV, Franques J, Guillevin R. et al. Revising the spectrum of lower motor neuron diseases with snake eyes appearance on magnetic resonance imaging. Euro J Neurol 2014; 21: 1233-1241
    CrossrefPubMedSearch in Google Scholar
  • 2 Sasaki S. Sporadic lower motor neuron disease with snake eyes appearance on the cervical horns by MRI. Cin Neurol Neurosurg 2015; 136: 122-131
    CrossrefPubMedSearch in Google Scholar
  • 3 Menon P, Kiernan MC, Vucic S. Cortical dysfunction underlies the development of the split-hand in anyotrophic lateral sclerosis. PLONSone 2014; 9: e87124
    CrossrefPubMedSearch in Google Scholar
  • 4 Bekci T, Yucel S, Aslam K. et al. “Snake eye” appearance on a teenage girl with spontaneous spinal ischemia. Spine 2015; 15: e45
    CrossrefPubMedSearch in Google Scholar
  • 5 Vishnu VY, Vinny PW, Modi M. et al. Snake eyes. Spine 205 15: 1484-1485
    CrossrefPubMed
  • 6 Mallio CA, Tombini M, Errante Y. et al. Progressive post-traumatic myelopathy presenting with magnetic resonance imaging snake-eye appearance. Spine 2013; 13: 830
    CrossrefPubMedSearch in Google Scholar
  • 7 Asaka T, Satake R, Takamori M. et al. Dissociated motor loss syndrome with cavities in the anterior horns. Internal Med 1995; 34: 1027-1029
    CrossrefPubMedSearch in Google Scholar
  • 8 Sharma S, Murgai A, Pankajakshan P. et al. Teaching NeuroImages: Snake eyes appearance in MRI in patients with ALS. Neurology 2013; 81: e29
    CrossrefPubMedSearch in Google Scholar
  • 9 Pradat P-F. Lower motor neuron syndrome with snake eyes appearance on MRI is a benign differential diagnosis of ALS and dysimmune neuropathies. Clin Neurol Neurosurg 2016; 141: 130
    CrossrefPubMedSearch in Google Scholar
  • 10 Kang JS, Jochem-Gawehn S, Laufs H. et al. Hirayama-Syndrom in Deutschland. Nervenarzt 2011; 82: 1264-1272
    CrossrefPubMedSearch in Google Scholar
  • 11 Kalita J, Kumar S, Misra UK. et al. Split hand index and ulnar to median ratio in Hirayama disease and amyotrophic lateral sclerosis. Amyotrop Lateral Scler frototemporal Degener 2017; 18: 598-603
    CrossrefPubMedSearch in Google Scholar
  • 12 Grimm A, Décard BF, Athanasopoulou I. et al. Nerve ultrasound for differentiation between amyotrophic lateral sclerosis and multifocal motor neuropathy. J Neurol 2015; 262: 870-880
    CrossrefPubMedSearch in Google Scholar
  • 13 DGN www.dgn.org/leitlinien/3012-ll-18-ll-amyotrophe-lateralsklerose-motoneuronerkrankungen