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Rofo 2022; 194(03): 310-312
DOI: 10.1055/a-1555-3762
The Interesting Case

Erdheim Chester Disease Mimicking Lymphoma: A Case Report

Philipp Moritz Wunschel
1   Radiology, Brüderkrankenhaus St. Josef, Paderborn, Germany
,
Wolfgang Voss
2   Pathology, Institut für Pathologie, Paderborn, Germany
,
Marc Keberle
3   Abt. Diagnostische Radiologie, Med. Hochschule Hannover, Paderborn, Germany
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Background

Erdheim Chester disease (ECD) is a rare disorder, characterized by organ infiltration of non-Langerhans cell foamy, CD68+, CD1a- histiocytes. Since first described in 1930 by William Chester, > 900 cases have been reported. The disease usually affects patients in the 5th – 7th decade of life with a predilection for males [1] [2] [3].



Publikationsverlauf

Artikel online veröffentlicht:
14. Oktober 2021

© 2021. Thieme. All rights reserved.

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