PDF herunterladen
Thromb Haemost 1970; 23(03): 449-454
DOI: 10.1055/s-0038-1654071
Originalarbeiten – Original Articles – Travaux Originaux
Schattauer GmbH

Cholecystectomy in a Patient with Hageman Trait

A Girolami
1   University of Padua Medical School, Institute of “Semeiotica Medica” (Director: Prof. M. Austoni), Padua
,
A Maffei   *
1   University of Padua Medical School, Institute of “Semeiotica Medica” (Director: Prof. M. Austoni), Padua
,
A Brunetti
1   University of Padua Medical School, Institute of “Semeiotica Medica” (Director: Prof. M. Austoni), Padua
,
M Lazzarin
1   University of Padua Medical School, Institute of “Semeiotica Medica” (Director: Prof. M. Austoni), Padua
› Institutsangaben
Weitere Informationen

Publikationsverlauf

Publikationsdatum:
27. Juni 2018 (online)

Auch verfügbar auf
    Lizenzen und Reprints

Summary

The case of a patient with Hageman trait who underwent cholecystectomy for cholelithiasis is reported. The surgical procedure was uneventful; no abnormal bleeding was noted during and after the operation. The transfusion of 4 cm3/kg b.w. of contacted 3-day old normal plasma corrected completely the coagulation abnormality. The glass and the silicone clotting times were slightly shortened even 64 h after the transfusion. The survival time for the infused factor XII activity resulted to be 41 h. 6 days after the plasma infusion the factor XII level was 1 % of normal. The significance of these findings is discussed.

* Of the Department of “Patologia Chirurgica”, University of Padua Medical School.


 

  • References

  • 1 Biggs R, Sharp A. A, Margolis J, Hardisty R. M, Stewart B. J, Davidson W. M. Defects in the early stages of blood coagulation: a report of four cases. Brit. J. Haemat 4: 177 1958;
    CrossrefPubMedSuche in Google Scholar
  • 2 Bok J, Veitkamp J. J, Loeliger E. A. Moderate factor XII deficiency. Thrombos. Diathes. haemorrh. (Stuttg.) 13: 8 1965;
    PubMedSuche in Google Scholar
  • 3 Botti R. E, Ratnoff O. D. Studies on the pathogenesis of thrombosis. An experimental hyper-coagulable state induced by the intravenous injection of ellagic acid. J. Lab. clin. Med 64: 385 1964;
    PubMedSuche in Google Scholar
  • 4 Caen J, Bernard J. Déficit en facteur Hageman. Rev. Hémat 13: 154 1958;
    PubMedSuche in Google Scholar
  • 5 Fantl P, Morris K. N, Sawers R. J. Repair of cardiac defect in patient with Ehlers-Danlos Syndrome and deficiency of Hageman factor. Brit. Med. J 1: 1202 1961;
    CrossrefPubMedSuche in Google Scholar
  • 6 Frick P. G, Hagen P. S. Severe coagulation defect without hemorrhagic symptoms caused by deficiency of the fifth plasma thromboplastin precursor. J. Lab. clin. Med 47: 592 1956;
    PubMedSuche in Google Scholar
  • 7 Girolami A, Cliffton E. E, Agostino D. The effect of ellagic acid on blood coagulation in vivo. Blood 27: 93 1966;
    PubMedSuche in Google Scholar
  • 8 Girolami A, Cliffton E. E. Hypercoagulable state in humans induced by the intravenous administration or purified ellagic acid. Thrombos. Diathes. haemorrh. (Stuttg.) 17: 165 1967;
    PubMedSuche in Google Scholar
  • 9 Girolami A, Scarpa R, Lazzarin M, Brunetti A. Coagulopatia da deficienza di fattore Hageman (Fattore XII). Prima osservazione in Italia. Riv. crit. Clin. med 3: 68 1968;
    PubMedSuche in Google Scholar
  • 10 Girolami A. Further studies on the ellagic acid induced hypercoagulable state. Lack of thrombosis in the dog after long-term administration of the compound. Coagulation 2: 263 1969;
    PubMedSuche in Google Scholar
  • 11 Gluech H. I, Roehll W. Myocardial infarction in a patient with Hageman (Faktor XII) defect. Ann intern. Med 64: 390 1966;
    CrossrefPubMedSuche in Google Scholar
  • 12 Haanen G, Hommes F, Benraad H, Morselt G. A case of Hageman-factor deficiency and a method to purify the factor. Thrombos. Diathes. haemorrh. (Stuttg.) 5: 201 1960;
    PubMedSuche in Google Scholar
  • 13 Hoak J. C, Swanson L. W, Warner E. P, Conner W. E. Myocardial infarction associated with severe factor XII deficiency. Lancet II: 884 1966;
    PubMedSuche in Google Scholar
  • 14 Jim R. T. S, Goldfein S. Hageman trait (Hageman factor deficiency). Amer. J. Med 23: 824 1957;
    CrossrefPubMedSuche in Google Scholar
  • 15 Kasper C. K, Whissell D. Y. E, Buechy P, Aggeler M. Hageman factor (factor XII) in an affected kindred and in normal adults. Brit. J. Haemat 14: 543 1968;
    CrossrefPubMedSuche in Google Scholar
  • 16 Kurkcuoglu M, Me Elfresh A. E. The Hageman factor : determinations of its concentrations during the neonatal period and presentation of a case of Hageman factor deficiency. J. Ped 57: 61 1960;
    CrossrefPubMedSuche in Google Scholar
  • 17 Larrieu M. J, Soulier J. P, Culot Y. Déficit en factor Hageman. Sang 28: 152 1957;
    PubMedSuche in Google Scholar
  • 18 Loeliger E. A, Hensen A. Coagulation studies in a case of Hageman trait. Thrombos. Diathes. haemorrh. (Stuttg.) 5: 187 1960;
    PubMedSuche in Google Scholar
  • 19 Miwa S, Asai I, Tsukada T, Shimisu-Teramura K, Sunaga Y. Hageman factor deficiency. Report of a case found in a Japanese girl. Acta haemat. (Basel) 39: 36 1968;
    CrossrefPubMedSuche in Google Scholar
  • 20 Ramot B, Singer K, Heller P, Zimmerman J. Hageman factor (HF) deficiency. Blood 2: 745 1956;
    PubMedSuche in Google Scholar
  • 21 Ratnoff O. D, Colopy J. E. A familial hemorrhagic trait associated with a deficiency of a clot-promoting fraction of plasma. J. clin. Invest 34: 602 1955;
    CrossrefPubMedSuche in Google Scholar
  • 22 Ratnoff O. D. Hageman trait. Thrombos. Diathes. hämorrh. (Stuttg.) 4 Suppl. 116 1960;
    PubMedSuche in Google Scholar
  • 23 Ratnoff O. D. Estimation of Hageman factor in plasma or plasma fractions. In: Blood coagulation, Hemorrhage and Thrombosis. Tocantins M. L, and Kazal L. A. (Editors). Grune and Stratton; New York: 1964
    Suche in Google Scholar
  • 24 Ratnoff O. D, Busse R. J, Sheon R. P. The demise of John Hageman. New Engl. J. Med 275: 760 1968;
    PubMedSuche in Google Scholar
  • 25 Ratnoff O. D. Personal communication.
    PubMed
  • 26 Sjolin K. E. The Hageman trait in a family with hemorrhagic diathesis. Acta genet. (Basel) 7: 54 1957;
    PubMedSuche in Google Scholar
  • 27 Thompson J. H, Spittel J. A, Pascuzzi C. A, Owen Ch. A. Laboratory and genetic observations in another family with the Hageman trait. Proc. Mayo Clin 35: 421 1963;
    PubMedSuche in Google Scholar
  • 28 Veltkamp J. J, Loeliger E. A, Hemker H. C. The biological half-life of Hageman factor. Thrombos. Diathes. hämorrh 13: 1 1965;
    PubMedSuche in Google Scholar