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DOI: 10.1055/s-0042-1755279
Vessel wall MRI in the dissecting pseudoaneurysm related to Parry-Romberg syndrome
Estudo de parede vascular por ressonância magnética em pseudoaneurisma dissecante associado a síndrome de Parry-RombergA 7-year-old girl with a previous diagnosis of Parry-Romberg syndrome presented with acute headache ([Figures 1] and [2]). Parry-Romberg syndrome is a subtype of localized scleroderma of the head that, although rare, may be associated with giant intracranial aneurysms.[1] The etiology of these aneurysms is still poorly understood; however, it is believed that it may be related to endothelial inflammatory injury or vasa vasorum microangiopathy and vascular wall ischemia.[1] [2] Dissecting pseudoaneurysm of intracranial arteries is rare and may result in acute headache and neurological deficits.[1] [2] The characterization of mural enhancement in vessel wall magnetic resonance imaging (MRI) in this case corroborated the hypothesis of a vasculitis-related etiology.
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Conflict of Interest
The authors have no conflict of interests to declare.
Authors' Contributions
AV: collected the data, conceived the analysis, and wrote and reviewed the paper; BCAT: guided the preparation of the work, and wrote and reviewed the paper.
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References
- 1 Bosman T, Van Bei Jnum J, Van Walderveen MAA, Brouwer PA. Giant intracranial aneurysm in a ten-year-old boy with parry romberg syndrome. A case report and literature review. Interv Neuroradiol 2009; 15 (02) 165-173
- 2 Kuechler D, Kaliaperumal C, Hassan A, Fanning N, Wyse G, O'Sullivan M. Aneurysmal subarachnoid haemorrhage in Parry-Rhomberg syndrome. BMJ Case Rep 2011; 2011: bcr1020114920
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Publication History
Received: 20 December 2021
Accepted: 06 February 2022
Article published online:
29 September 2022
© 2022. Academia Brasileira de Neurologia. This is an open access article published by Thieme under the terms of the Creative Commons Attribution 4.0 International License, permitting copying and reproduction so long as the original work is given appropriate credit (https://creativecommons.org/licenses/by/4.0/)
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References
- 1 Bosman T, Van Bei Jnum J, Van Walderveen MAA, Brouwer PA. Giant intracranial aneurysm in a ten-year-old boy with parry romberg syndrome. A case report and literature review. Interv Neuroradiol 2009; 15 (02) 165-173
- 2 Kuechler D, Kaliaperumal C, Hassan A, Fanning N, Wyse G, O'Sullivan M. Aneurysmal subarachnoid haemorrhage in Parry-Rhomberg syndrome. BMJ Case Rep 2011; 2011: bcr1020114920