Journal of Pediatric Neurology 2024; 22(01): 072-076
DOI: 10.1055/s-0043-1761483
Case Report

Reversible Cerebral Vasoconstriction Syndrome with Intracerebral Hemorrhage in a Thalassemic Child—An Extremely Rare Complication

1   Department of Neuromedicine, Bangur Institute of Neurosciences, Kolkata, West Bengal, India
,
Atanu Biswas
1   Department of Neuromedicine, Bangur Institute of Neurosciences, Kolkata, West Bengal, India
,
Uma Sinha Roy
1   Department of Neuromedicine, Bangur Institute of Neurosciences, Kolkata, West Bengal, India
,
Biman Kanti Ray
1   Department of Neuromedicine, Bangur Institute of Neurosciences, Kolkata, West Bengal, India
› Author Affiliations

Abstract

A 6-year-old known thalassemic boy presented with a posttransfusional thunderclap headache. A computed tomography scan showed left occipital lobar bleed and magnetic resonance angiography showed diffuse cerebral vasoconstriction, which resolved after 3 months, suggesting reversible cerebral vasoconstriction syndrome. He was treated with oral nimodipine for 3 months and had an excellent recovery without sequelae. To the best of the authors' knowledge, the index case is the first reported case of reversible cerebral vasoconstriction syndrome in a thalassemic child.



Publication History

Received: 22 September 2022

Accepted: 28 December 2022

Article published online:
06 February 2023

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