Zusammenfassung
Wir berichten über den seltenen Fall eines Lymphangiomyoms des Ileum-Mesenteriums bei einer 16jährigen Patientin, die wegen unklarer Anämie (Hb 4,3 g%), Belastungsdyspnoe, Leistungsabfall und Schwindel von einem auswärtigen Krankenhaus zugewiesen wurde.
Abstract
We describe a 16-year-old female with a lymphangiomyoma of the ileal mesentery. The patient presented with anemia, shortness of breath, fatigue, and vertigo. Sonography showed a 13-cm mass in the lower abdomen. Laparoscopy showed a tumor in the mesentery of the terminal ileum. Laparotomy was performed to resect the mass with a segment of the ileum. Histology showed a lymphangiomyoma.
Literatur
-
01
Berger, U., , Khaghani, A. , Pomerance, A. , Yacoub, M. H. , Coombes R. C. .
Pulmonary lymphangioleiomyomatosis and steroid receptors. An immunohistochemical study.
Amer. J. Clin. Pathol..
93 (5)
1990;
609
-
02
Bhattacharaya, A. K..
Retroperitoneal Lymphangiomyoma. A 36-year benign course in a postmenopausal women.
Cancer.
56
1985;
1144
-
03
Bjornland, K..
Acute abdominal pain as presenting symptom in lymphangioleiomyomatosis.
Europ. J. Surg..
157
1991;
367
-
04
Capron, F., , Ameille, J. , Leclerc P. .
Pulmonary lymphangioleiomyomatosis and Bourneville's tuberous sclerosis with pulmonary involvement: the same disease?.
Cancer.
52
1983;
851
-
05
Ernst, J. C., , Sohaey, J. R. , Cary J. M. .
Pelvic lymphangioleiomyomatosis. Atypical precursor to pulmonary disease.
Chest.
106 (4)
1994;
1267
-
06
Fuchs, J., , Maschek, H. , von Schweinitz, D. , Gluer, S. , Mildenberger H. .
Retroperitoneal lymphangiomyoma in an infant.
Europ. J. Pediatr. Surg..
7 (2)
1997;
112
-
07
Hansen, P. S..
Hemangioma of the small intestine.
Amer. J. Clin. Pathol..
48
1948;
18
-
08
Ouakdi, M..
Retroperitoneal Lymphangioleiomyoma. Apropos of a new case.
J. Urol..
95
1989;
103
-
09
Peyrol, S., , Gindre, D. , Cordier, J. F. , Loire, R. , Grimaud J. A. .
Characterization of the smooth muscle cell infiltrate and associated connective matrix of lymphangiomyomatosis. Immunohistochemical and ultrastructural study of two cases.
J. Pathol..
168 (4)
1992;
387
-
10
Scully, R. E., , Mark, E. J. , McNeely, W. F. , McNeely B. U. .
Case records of the Massachusetts General Hospital.
New Engl. J. Med..
330 (18)
1994;
1300
-
11
Sinclair, W., , Wright, J. L. , Churg A. .
Lymphangioleiomyomatosis presenting in a postmenopausal woman.
Thorax.
40
1985;
475
-
12
Taylor, J. R., , Ryu, J. , Colby, T. V. , Raffin T. A. .
Lymphangioleiomyomatosis. Clinical course in 32 patients.
New Engl. J. Med..
323 (18)
1990;
1254
-
13
Wolff, M..
Lymphangiomyoma: clinicopathologic study and ultrastructural confirmation of its histogenesis.
Cancer.
31
1973;
988
Dr. PD Martin Kolben
Frauenklinik der TU München Klinikum rechts der Isar
Ismaninger Straße 22
81675 München