Hepatic Weber-Christian Disease

Jared M. Wasserman; Swan N. Thung; Richard Berman; Henry C. Bodenheimer Jr; Samuel H. Sigal

doi:10.1055/s-2001-12934

Seminars in Liver Disease, Inhaltsverzeichnis

Semin Liver Dis 2001; 21(1): 115-118
DOI: 10.1055/s-2001-12934

Diagnostic Problems in Hepatology
Copyright © 2001 by Thieme Medical Publishers, Inc., 333 Seventh Avenue, New York, NY 10001, USA. Tel.: +1(212) 584-4662

Hepatic Weber-Christian Disease

Jared M. Wasserman² , Swan N. Thung³ , Richard Berman⁴ , Henry C. Bodenheimer, Jr.^1,2 , Samuel H. Sigal^1,2

¹Division of Liver Diseases, Mount Sinai School of Medicine of New York University, New York, NY
²Department of Medicine, Mount Sinai School of Medicine of New York University, New York, NY
³Department of Pathology, Mount Sinai School of Medicine of New York University, New York, NY
⁴Brookhaven Memorial Hospital Medical Center, Patchogue, NY

Abstract

ABSTRACT

Weber-Christian disease is an idiopathic disorder characterized by nonsuppurative nodular panniculitis with a lobular distribution of acute inflammation in the subcutaneous fat with occasional systemic involvement. Although the histopathologic features of the liver disease in the syndrome are characterized by steatohepatitis, the clinical features have not been well defined. We report a case of hepatic Weber-Christian disease and discuss the clinical differences from steatohepatitis due to the more common disorders of obesity and diabetes mellitus.

KEYWORD

Weber-Christian disease - steatohepatitis - liver

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Referenzen

REFERENCES

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