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Neuropediatrics 2004; 35(4): 253-254
DOI: 10.1055/s-2004-820995
Short Communication

Georg Thieme Verlag KG Stuttgart · New York

Acute Disseminated Encephalomyelitis and Mucocutaneous Ulcerations

G. M. Lackmann1 , S. Lyding2 , A. Scherer3 , T. Niehues2
  • 1Outpatient Paediatric Office, Hamburg, Germany
  • 2Department of Paediatric Oncology, Haematology and Immunology, Division of Paediatric Immunology and Rheumatology, Heinrich-Heine University, Düsseldorf, Germany
  • 3Institute of Diagnostic Radiology, Heinrich-Heine University, Düsseldorf, Germany
Further Information

Publication History

Received: October 12, 2003

Accepted after Revision: April 9, 2004

Publication Date:
10 August 2004 (online)

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Abstract

A 15-year-old Libyan girl developed typical findings of acute disseminated encephalomyelitis, unveiling characteristic symptoms of Behçet's disease by months. This disease course of neuro-Behçet's disease is quite exceptional in children, and an isolated, high-density MRI lesion of the corpus callosum, like in the present case, has not been described in neuro-Behçet's disease before.

Key words

Acute disseminated encephalomyelitis - Behçet's disease - multiple sclerosis - MRI lesions - corpus callosum - oral and genital ulcers

References

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Priv.-Doz. Dr. med. Gerd-Michael Lackmann

Reinstorfweg 10 a

21107 Hamburg

Germany

Email: GMLackmann.Praxis@t-online.de