Congenital Orbital Teratoma

Con Sreenan; Royce Johnson; Laurie Russell; Ravi Bhargava; Horacio Osiovich

doi:10.1055/s-2007-993867

American Journal of Perinatology, Table of Contents

Am J Perinatol 1999; 16(5): 251-255
DOI: 10.1055/s-2007-993867

ORIGINAL ARTICLE

Congenital Orbital Teratoma

Con Sreenan¹ , Royce Johnson² , Laurie Russell³ , Ravi Bhargava⁴ , Horacio Osiovich¹

¹Neonatal Intensive Care Unit, Royal Alexandra Hospital, Edmonton, Alberta, Canada
²Department of Ophthalmology, Royal Alexandra Hospital, Edmonton, Alberta, Canada
³Department of Pathology, Royal Alexandra Hospital, Edmonton, Alberta, Canada
⁴Department of Radiology, University of Alberta Hospital, Edmonton, Alberta, Canada

Abstract

ABSTRACT

A case of congenital orbital teratoma is described in which there was no organized eye only microscopic evidence of ocular tissues within the disorganized teratoma. A baby boy presented at birth with a 10-X-8-cm mass extruding from the left orbit. Magnetic resonance imaging (MRI) showed a mixed cystic-solid orbital mass containing areas of calcification and deforming the bony orbit around its margins. There was no organized eye and no intracranial extension. The eye was removed with reconstruction of the eyelids. Histopathology showed representation from all three germ cell layers consistent with a teratoma. There was no organized eye, but some disorganized ocular structures within the teratoma. Follow-up has been uneventful. Neo-natologists and pediatricians should be aware of the possible diagnoses in a newborn presenting with an orbital mass, so that early definitive surgery can be performed with preservation of the globe where possible.

Keywords

Congenital orbital teratoma

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