Subscribe to RSS

DOI: 10.1590/0004-282X20150155
Sneddon syndrome – imaging findings
Síndrome de Sneddon – achados de imagemThe Sneddon syndrome is a rare clinical syndrome that associates strokes and livedo, etiologically related with the antiphospholipid antibody syndrome ([Figure 1])[1],[2],[3],[4],[5].


This 42 year-old woman with headache and right hemiparesis had a MRI that showed acute/ subacute ischemia in part of the territory of the left middle cerebral artery (MCA) and bi-hemispheric gliosis/ encephalomalacia ([Figure 2]). MR angiography showed normal cervical carotid and vertebral circulation, filling defect in M2 segment of the left MCA. Catheter angiography disclosed difuse cortical occlusive arteriopathy associated with a rich collateral cortical network. The M2 occlusion was reperfused, with infarct sign in its territory ([Figures 3] and [4]).






#
Conflicts of interest:
There is no conflict of interest to declare.
-
References
- 1 Maamar M, Rahmani M, Aidi S, Benabdeljlil M, El HassaniMy R, Jiddane M et al. [Sneddon’s syndrome: 15 cases with cerebral angiography]. Rev Neurol (Paris). 2007;163(8-9):809-16. French. doi:10.1016/S0035-3787(07)91463-0
- 2 Marinho JL, Piovesan EJ, Leite Neto MP, Kotze LR, Noronha L, Twardowschy CA et al. Clinical, neurovascular and neuropathological features in Sneddon’s syndrome. ArqNeuropsiquiatr. 2007;65(2B):390-5. doi:10.1590/S0004-282X2007000300005
- 3 Boesch SM, Plörer AL, Auer AJ, Poewe W, Aichner FT, Felber SR et al. The natural course of Sneddon syndrome: clinical and magnetic resonance imaging findings in a prospective six year observation study. J Neurol Neurosug Psychiatry. 2003;74(4):542-4. doi:10.1136/jnnp.74.4.542
- 4 Stockhammer G, Felber SR, Zelger B, Sepp N, Birbamer GG, Fritsch PO et al. Sneddon’s syndrome: diagnosis by skin biopsy and MRI in 17 patients. Stroke.1993;24(5):685-90. doi:10.1161/01.STR.24.5.685
- 5 Uthman, I.W., Khamashta, M.A. Livedo racemosa: a striking dermatological sign for the antiphospholipid syndrome [Editorial]. J Rheumatol. 2006;33(12):2379-82.
Address for correspondence
Publication History
Received: 11 July 2015
Accepted: 04 August 2015
Article published online:
06 September 2023
© 2015. Academia Brasileira de Neurologia. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commecial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)
Thieme Revinter Publicações Ltda.
Rua do Matoso 170, Rio de Janeiro, RJ, CEP 20270-135, Brazil
-
References
- 1 Maamar M, Rahmani M, Aidi S, Benabdeljlil M, El HassaniMy R, Jiddane M et al. [Sneddon’s syndrome: 15 cases with cerebral angiography]. Rev Neurol (Paris). 2007;163(8-9):809-16. French. doi:10.1016/S0035-3787(07)91463-0
- 2 Marinho JL, Piovesan EJ, Leite Neto MP, Kotze LR, Noronha L, Twardowschy CA et al. Clinical, neurovascular and neuropathological features in Sneddon’s syndrome. ArqNeuropsiquiatr. 2007;65(2B):390-5. doi:10.1590/S0004-282X2007000300005
- 3 Boesch SM, Plörer AL, Auer AJ, Poewe W, Aichner FT, Felber SR et al. The natural course of Sneddon syndrome: clinical and magnetic resonance imaging findings in a prospective six year observation study. J Neurol Neurosug Psychiatry. 2003;74(4):542-4. doi:10.1136/jnnp.74.4.542
- 4 Stockhammer G, Felber SR, Zelger B, Sepp N, Birbamer GG, Fritsch PO et al. Sneddon’s syndrome: diagnosis by skin biopsy and MRI in 17 patients. Stroke.1993;24(5):685-90. doi:10.1161/01.STR.24.5.685
- 5 Uthman, I.W., Khamashta, M.A. Livedo racemosa: a striking dermatological sign for the antiphospholipid syndrome [Editorial]. J Rheumatol. 2006;33(12):2379-82.







