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CC BY-NC-ND 4.0 · Arq Neuropsiquiatr 2017; 75(02): 130-131
DOI: 10.1590/0004-282X20160198
IMAGES IN NEUROLOGY

Eagle’s syndrome: a pain in the neck

Síndrome de Eagle: um diagnóstico difícil
Leonardo Cordenonzi Pedroso de Albuquerque
1   Universidade Federal do Rio Grande do Sul, Hospital de Clínicas de Porto Alegre, Divisão de Neurologia, B.R.A.I.N. (Basic Research and Advanced Investigations in Neurology), Porto Alegre RS, Brasil;
,
Juliana Ávila Duarte
2   Hospital de Clínicas de Porto Alegre, Serviço de Radiologia e Diagnóstico por Imagem, Porto Alegre RS, Brasil.
,
Amalia Izaura Nair Medeiros Klaes
2   Hospital de Clínicas de Porto Alegre, Serviço de Radiologia e Diagnóstico por Imagem, Porto Alegre RS, Brasil.
,
Suelen Mandelli Mota
1   Universidade Federal do Rio Grande do Sul, Hospital de Clínicas de Porto Alegre, Divisão de Neurologia, B.R.A.I.N. (Basic Research and Advanced Investigations in Neurology), Porto Alegre RS, Brasil;
,
Bárbara Reis Krammer
1   Universidade Federal do Rio Grande do Sul, Hospital de Clínicas de Porto Alegre, Divisão de Neurologia, B.R.A.I.N. (Basic Research and Advanced Investigations in Neurology), Porto Alegre RS, Brasil;
,
Larissa Bianchini
1   Universidade Federal do Rio Grande do Sul, Hospital de Clínicas de Porto Alegre, Divisão de Neurologia, B.R.A.I.N. (Basic Research and Advanced Investigations in Neurology), Porto Alegre RS, Brasil;
,
Marino Muxfeldt Bianchin
1   Universidade Federal do Rio Grande do Sul, Hospital de Clínicas de Porto Alegre, Divisão de Neurologia, B.R.A.I.N. (Basic Research and Advanced Investigations in Neurology), Porto Alegre RS, Brasil;
› Author Affiliations
Support: Brazilian Government research grant agencies CNPq, FAPERGS and FIPE/HCPA. Bianchin MM is further supported by CNPq (#307084/2014-0).
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A 60-year-old male patient was evaluated for cervical pain, hiccups, dysphonia and dysphagia for five months. Physical examination showed left IX and X cranial nerve palsy. Brain MRI was normal. A cervical CT scan showed an elongated styloid process and stylohyoid ligament pseudoarthrosis ([Figure]). Eagle’s syndrome is a rare entity caused by abnormal enlargement and ossification of the styloid process, the attached stylohyoid ligament and the lesser cornu of the hyoid bone[1],[2],[3],[4]. The condition causes variable degrees of compression of V, VII, IX, X and XII cranial nerves, and the jugular or carotid, leading to diverse symptoms[1],[2],[3],[4]. Eagle’s syndrome pathogenesis remains unclear[1],[2],[3],[4].

Zoom Image
Figure Maximum intensity projection and 3D CT-scan volume rendering of the patient’s cervical region. Note bilateral calcification of the stylohyoid ligament.

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Conflict of interest:

There is no conflict of interest to declare.

Support:

Brazilian Government research grant agencies CNPq, FAPERGS and FIPE/HCPA. Bianchin MM is further supported by CNPq (#307084/2014-0).


  • References

  • 1 Bahgat M, Bahgat Y, Bahgat A. Eagle’s syndrome, a rare cause of neck pain. BMJ Case Rep. 2012; pii: bcr2012006278. http://doi.org/10.1136/bcr-2012-006278
  • 2 Costantinides F, Vidoni G, Bodin C, Di Lenarda R. Eagle’s syndrome: signs and symptoms. Cranio.. 2013;31(1):56-60. http://doi.org/10.1179/crn.2013.008
  • 3 Fusco DJ, Asteraki S, Spetzler RF. Eagle’s syndrome: embryology, anatomy, and clinical management. Acta Neurochir (Wien). 2012;154(7):1119-26. http://doi.org/10.1007/s00701-012-1385-2
  • 4 Piagkou M, Anagnostopoulou S, Kouladouros K, Piagkos G. Eagle’s syndrome: a review of the literature. Clin Anat. 2009;22(5):545-58. http://doi.org/10.1002/ca.20804

Address for correspondence

Marino M. Bianchin
B.R.A.I.N. Experimental Research Centre, Hospital de Clínicas de Porto Alegre; Rua Ramiro Barcelos, 2350; 90035-903 Porto Alegre RS
Brasil   

Publication History

Received: 17 August 2016

Accepted: 10 October 2016

Article published online:
05 September 2023

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  • References

  • 1 Bahgat M, Bahgat Y, Bahgat A. Eagle’s syndrome, a rare cause of neck pain. BMJ Case Rep. 2012; pii: bcr2012006278. http://doi.org/10.1136/bcr-2012-006278
  • 2 Costantinides F, Vidoni G, Bodin C, Di Lenarda R. Eagle’s syndrome: signs and symptoms. Cranio.. 2013;31(1):56-60. http://doi.org/10.1179/crn.2013.008
  • 3 Fusco DJ, Asteraki S, Spetzler RF. Eagle’s syndrome: embryology, anatomy, and clinical management. Acta Neurochir (Wien). 2012;154(7):1119-26. http://doi.org/10.1007/s00701-012-1385-2
  • 4 Piagkou M, Anagnostopoulou S, Kouladouros K, Piagkos G. Eagle’s syndrome: a review of the literature. Clin Anat. 2009;22(5):545-58. http://doi.org/10.1002/ca.20804

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Zoom Image
Figure Maximum intensity projection and 3D CT-scan volume rendering of the patient’s cervical region. Note bilateral calcification of the stylohyoid ligament.