Die IgA(Purpura Schönlein-Henoch)-Vaskulitis

ZUSAMMENFASSUNG

Die IgA-Vaskulitis (früher Purpura Schönlein-Henoch) ist eine systemische, immunkomplexvermittelte Vaskulitis der kleinen Gefäße, die gekennzeichnet ist durch die klinische Trias aus palpabler Purpura, Bauch- und Gelenkschmerzen. Es ist die häufigste Vaskulitis im Kindes- und Jugendalter. Die Diagnose ist klinisch zu stellen. Die kutane Vaskulitis zeigt überwiegend eine Spontanremission. Die Nieren sind häufig und in unterschiedlichem Ausmaß betroffen. Bei schweren Verläufen können ein akutes Nierenversagen und ein nephrotisches Syndrom auftreten sowie renale Langzeitschäden verbleiben.

Schlüsselwörter

IgA-Vaskulitis - Diagnostik - IgA-Vaskulitis - Steroide - Vaskulitis-Klassifikation - IgA-Nephritis - Haut-Vaskulitis

Publikationsverlauf

Artikel online veröffentlicht:
06. September 2024

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