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CC BY 4.0 · European J Pediatr Surg Rep. 2024; 12(01): e77-e80
DOI: 10.1055/a-2448-3530
Case Report

Successful Repair of Esophageal Atresia with Tracheoesophageal Fistula and Interrupted Inferior Vena Cava: A Rare Case Report

Xiao Long Mu 
1   Department of Pediatrics, Pediatric Surgery, Taihe Hospital, Shiyan, Hubei, People's Republic of China
,
Junqiu Wang
2   Department of Dermatology, Taihe Hospital, Shiyan, Hubei, People's Republic of China
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Abstract

Esophageal atresia (EA) with tracheoesophageal fistula (TEF) is a congenital anomaly that can present complex surgical challenges, especially when accompanied by rare vascular conditions like an interrupted inferior vena cava (IVC). The division of the azygos vein is a common part of TEF repair, but in the presence of an interrupted IVC, this can lead to life-threatening complications. We report the case of a newborn diagnosed with EA, TEF, and interrupted IVC, successfully treated through thoracotomy. This case underscores the importance of prenatal and postnatal imaging to diagnose vascular anomalies prior to TEF repair, ensuring the preservation of the azygos vein to prevent fatal outcomes. Raising awareness of this rare association is crucial to optimizing surgical planning and outcomes.

Keywords

esophageal atresia - tracheoesophageal fistula - interrupted inferior vena cava

Supplementary Material



Publication History

Received: 10 April 2024

Accepted: 19 October 2024

Accepted Manuscript online:
23 October 2024

Article published online:
18 November 2024

© 2024. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution License, permitting unrestricted use, distribution, and reproduction so long as the original work is properly cited. (https://creativecommons.org/licenses/by/4.0/)

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