Covered Bladder Exstrophy with Scrotal Duplication

Introduction

Bladder exstrophy is a rare condition, with an incidence of 3.3 per 100 000 newborns [8]. Exstrophic anomalies can be classified into four main types: isolated epispadias, classical bladder exstrophy, cloacal exstrophy and exstrophy variants. Exstrophy variants consist of covered bladder exstrophy, also referred to as pseudoexstrophy, duplicate exstrophy and superior vesical fissure [1] [2] [9]. These variants of classical bladder exstrophy represent a rare subgroup of anomalies that all have a split symphysis and divergent rectus muscles as the main feature in common [9]. We report here the case of a boy with covered bladder exstrophy and scrotal duplication.

References

• 1 Boemers TM, de Jong TPVM, Rövekamp MH. et al . Covered exstrophy associated with an anorectal malformation: a rare variant of classical bladder exstrophy.  Pediatr Surg Int. 1994;  9 438-440
• 2 Boemers TM, de Jong TPVM, Vegt PDJ. et al . Duplicate exstrophy. Report of a case and review of the literature.  Pediatr Surg Int. 1995;  10 183-185
• 3 Borwankar SS, Kasat LS, Naregal A. et al . Covered exstrophy: a rare variant.  Pediatr Surg Int. 1998;  14 129-130
• 4 Chadha R, Sharma A, Bagga D. et al . Pseudoexstrophy associated with congenital pouch colon.  J Pediatr Surg. 1998;  33 1831-1833
• 5 Chadha R, Sharma A, Bagga D. et al . Covered exstrophy with incomplete duplication of the bladder.  Pediatr Surg Int. 1999;  15 422-424
• 6 Lowentritt BH, van Zijl PS, Frimberger D. et al . Variants of the exstrophy complex: a single institution experience.  J Urol. 2005;  173 1732-1737
• 7 Marshall VF, Muecke EC. Variations in exstrophy of the bladder.  J Urol. 1962;  92 766-796
• 8 Rock S, Gearhart J. et al . Complete lower urinary tract duplication with true diphallia presenting as a rare covered exstrophy variant.  J Urol. 1997;  157 1907-1908
• 9 Turner WR, Ransley PG, Bloom DA. et al . Variants of the exstrophic complex.  Urol Clin N Amer. 1980;  7 493-501

Correspondence