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DOI: 10.1055/s-0030-1250102
© Georg Thieme Verlag KG Stuttgart · New York
Cardiac Defect with Diaphragmatic Hernia and Left Lung Agenesis – Heart Disease and Other Anomalies
Publikationsverlauf
received February 10, 2010
Publikationsdatum:
04. Oktober 2010 (online)
![](https://www.thieme-connect.de/media/thoracic/201007/lookinside/thumbnails/10.1055-s-0030-1250102-1.jpg)
Abstract
This report describes a rare case of left pulmonary agenesis associated with congenital diaphragmatic hernia and congenital heart disease in a 2-year-old child with pulmonary hypertension. We performed direct radical correction of the congenital heart defect. The postoperative course was challenging but without major complications.
Key words
Cardiovascular surgery - thoracic surgery - heart disease - congenital heart disease - lung agenesis‐diaphragmatic hernia - sildenafil
References
- 1 Graziano J N Congenital Diaphragmatic Hernia Study Group for the . Cardiac anomalies in patients with congenital diaphragmatic hernia and their prognosis: a report from the Congenital Diaphragmatic Hernia Study Group. Journal of Pediatric Surgery. 2005; 40 1045-1050
- 2 Finci V, Begbetti M, Kalangos A, Brundler M A. Unilateral total and contralateral partial pulmonary agenesis associated with total anomalous pulmonary venous drainage. J Pediatr. 1999; 134 510-512
- 3 Ishikawa K, Hoshino S, Iwaya F, Ono T, Sato K, Misawa Y. A case of ventricular septal defect and atrial septal defect in an infant with right lung aplasia. Jpn J Cardiovasc Surg. 1999; 28 163-166
- 4 Buzzarro M, Gross I. Inhaled nitric oxide for the postoperative management of pulmonary hypertension in infants and children with congenital heart disease. Anesth Analg. 2006; 102 (3) 964
- 5 Mikhail G W, Prasad S K, Li W, Rogers P, Chester A H, Bayne S, Stephens D, Khan M, Gibbs J S R, Evans T W, Mitchell A, Yacoub M H, Gatzoulis M A. Clinical and haemodynamic effects of sildenafil in pulmonary hypertension: acute and mid-term effects. European Heart Journal. 2004; 25 431-436
- 6 Sastry B K, Narasimhan C, Reddy N K, Raju B S. Clinical efficacy of sildenafil in primary pulmonary hypertension: a randomized, placebo-controlled, double-blind, crossover study. J Am Coll Cardiol. 2004; 43 1149-1153
Dr. Raffaele Giordano, MD
Department of Clinical Medicine and Cardiovascular Sciences, Adult and Pediatric Cardiac Surgery
University of Naples Federico II
Via G. Filangieri 125/A
84013 Cava de' Tirreni
Italy
Telefon: +39 32 97 09 95 40
Fax: +39 08 17 46 26 36
eMail: raf_jordan@inwind.it