European J Pediatr Surg Rep. 2015; 03(01): 030-032
DOI: 10.1055/s-0034-1382821
Case Report
Georg Thieme Verlag KG Stuttgart · New York

Dumbbell-Shaped Rhabdomyosarcoma: Two-Stage Surgical Resection

Mahmoud ElFiky
1   Department of Pediatric Surgery, Cairo University, Cairo, Egypt
› Author Affiliations
Further Information

Publication History

21 February 2014

02 April 2014

Publication Date:
17 July 2014 (online)

Abstract

Female neonate admitted to our hospital with an abdominal mass and a thigh mass that were connected as a single dumbbell-shaped mass. CT was done on admission that showed cystic swelling in the thigh with intra-abdominal extension passing under inguinal ligament, most probably lymphangioma.

The patient was assessed and prepared for surgery starting with the abdominal part then after two days for the thigh mass. Distal pulses in the lower limbs were assessed intra- and postoperatively following both surgeries. The pathology report showed rhabdomyosarcoma of the embryonal type.

 
  • References

  • 1 Lobe TE, Wiener ES, Hays DM , et al. Neonatal Rhabdomyosarcoma: The IRS Experience. J Pediatr Surg 1994; 29 (8) 1167-1170 . doi:10.1016/0022-3468(94)90302-6
  • 2 Xue H, Horwitz JR, Smith MB , et al. Malignant solid tumors in neonates: a 40-year review. J Pediatr Surg 1995; 30 (4) 543-545
  • 3 Moore SW, Kaschula ROC, Albertyn R , et al. The outcome of solid tumours occurring in the neonatal period. Pediatr Surg Int 1995; 10: 366-370
  • 4 Aquino MR, Gibson DP, Bloom DA. Paratesticular rhabdomyosarcoma with metastatic encasement of the abdominal aorta. Pediatr Radiol 2011; 41 (8) 1061-1064
  • 5 Raney Jr RB, Hays DM, Tefft M , et al. Rhabdomyosarcoma and the undifferentiated sarcomas. In: Pizzo PA, Poplack DG, , eds. Principles and Pactice of Pediatric Oncology. Philadelphia, PA: Lippincott; 1989: 635-658
  • 6 Dillon PW, Whalen TV, Azizkhan RG , et al; Children's Cancer Group Surgical Committee. Neonatal soft tissue sarcomas: the influence of pathology on treatment and survival. J Pediatr Surg 1995; 30 (7) 1038-1041
  • 7 Barr FG. Molecular genetics and pathogenesis of rhabdomyosarcoma. J Pediatr Hematol Oncol 1997; 19 (6) 483-491
  • 8 Richard G. Azizkhan, Perinatal tumors. In: Carachi R, Grosfeld JL, Azmy AF, , eds. The Surgery of Childhood Tumors. 2nd ed. Berlin, Heidelberg: Springer-Verlag; 2008: 146
  • 9 Crist W, Gehan EA, Ragab AH , et al. The Third Intergroup Rhabdomyosarcoma Study. J Clin Oncol 1995; 13 (3) 610-630
  • 10 Crist WM, Anderson JR, Meza JL , et al. Intergroup rhabdomyosarcoma study-IV: results for patients with nonmetastatic disease. J Clin Oncol 2001; 19 (12) 3091-3102
  • 11 Büyükpamukçu M, Varan A, Tanyel C , et al. Solid tumors in the neonatal period. Clin Pediatr (Phila) 2003; 42 (1) 29-34
  • 12 Ferrari A, Casanova M, Bisogno G , et al; Italian Cooperative Group. Rhabdomyosarcoma in infants younger than one year old: a report from the Italian Cooperative Group. Cancer 2003; 97 (10) 2597-2604