Abstract
Idiopathic intracranial hypertension (IIH) is a rare disorder occurring more frequently
in obese women of childbearing age, resulting in increased intracranial pressure (ICP)
from an unknown cause. Recent advances in epidemiology, imaging, and treatment have
provided a better understanding of IIH in recent years, with better identification
of visual risk factors and atypical forms of IIH, including fulminant IIH and spontaneous
cerebrospinal fluid leaks, and a randomized clinical trial providing the rationale
for the use of acetazolamide. In addition, a revised version of the modified Dandy
criteria for the diagnosis of IIH was suggested in 2013, with better definition of
IIH in adults and children; however, controversy regarding nomenclature has precluded
its acceptance among IIH experts. Finally, questions regarding the best surgical strategy,
the indications for venous sinus stenting, and the diagnostic role of the radiologic
findings commonly seen in IIH have remained unanswered.
Keywords
idiopathic intracranial hypertension - modified Dandy criteria - cerebrospinal fluid
- papilledema - acetazolamide
