Abstract
Choledochal cyst (CC) is an important surgical cause of jaundice in infants. Infantile
variant of CC can mimic biliary atresia in clinical presentation. CC associated with
biliary atresia is well described in literature. We encountered an atretic variant
of CC that has not been described in literature ever. The characteristics of this
unusual case, management, and proposed hypothesis to its pathogenesis are discussed
here.
Keywords
choledochal cyst - cystic biliary atresia - atretic variant