Skip Segment Hirschsprung Disease Managed by Pull-Through of the Right Colon

Hira Ahmad; Alejandra Vilanova-Sánchez; Isabel Amengual; Laura Guerra-Pastrian; Marta Garrido-Pontnou; Cristina Montalvo; Alba Bueno; Jacob Langer; Richard J. Wood; Marc A. Levitt

doi:10.1055/s-0041-1726347

European Journal of Pediatric Surgery Reports, Table of Contents

CC BY 4.0 · European J Pediatr Surg Rep. 2021; 09(01): e28-e32
DOI: 10.1055/s-0041-1726347

Case Report

Skip Segment Hirschsprung Disease Managed by Pull-Through of the Right Colon

Hira Ahmad

¹Department of Pediatric Colorectal and Pelvic Reconstructive Surgery, Nationwide Children's Hospital Columbus, Ohio, United States

,

Alejandra Vilanova-Sánchez

²Colorectal and Urogenital Reconstruction Unit, La Paz University Hospital, Madrid, Spain

,

Isabel Amengual

³Department of Pathology, Son Espases University Hospital, Palma de Mallorca, Illes Balears, Spain

,

Laura Guerra-Pastrian

⁴Department of Pathology, La Paz University Hospital, Madrid, Madrid, Spain

,

Marta Garrido-Pontnou

⁵Department of Pathology, Vall d'Hebron Hospital Universitari, Barcelona, Catalunya, Spain

,

Cristina Montalvo

⁶Department of Pediatric Surgery, Son Espases University Hospital, Palma de Mallorca, Illes Balears, Spain

,

Alba Bueno

⁷Department of Pediatric Surgery, Hospital Universitario La Paz, Paseo de la Castellana 261, Madrid, Madrid, Spain

,

Jacob Langer

¹Department of Pediatric Colorectal and Pelvic Reconstructive Surgery, Nationwide Children's Hospital Columbus, Ohio, United States

⁸Division of General and Thoracic Surgery, SickKids, Toronto, Ontario, Canada

,

Richard J. Wood

¹Department of Pediatric Colorectal and Pelvic Reconstructive Surgery, Nationwide Children's Hospital Columbus, Ohio, United States

,

Marc A. Levitt

⁹Division of Colorectal and Pelvic Reconstructive Surgery, Children's National Medical Center, Washington, District of Columbia, United States

› Author Affiliations

Abstract

Hirschsprung disease is the most common neurocristopathy in children, resulting in the congenital loss of enteric ganglia. Rare reports of skip lesions have previously been reported in the literature. We present a case of skip lesions known prior to surgery and managed by pull-through of the right colon that allowed the preservation of the colon.

Keywords

calretinin stain - reoperation - enterocolitis - continence - aganglionosis

Full Text

References

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