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CC BY 4.0 · European J Pediatr Surg Rep. 2021; 09(01): e46-e49
DOI: 10.1055/s-0041-1728724
Case Report

Posterior Cloacal Variant with Clitorolabial Transposition and a Rectoperineal Fistula

Niveshni Maistry
1   Department of Paediatric Surgery, Chris Hani Baragwanath Hospital, Diepkloof, Soweto, Gauteng, South Africa
,
Giulia Brisighelli 
1   Department of Paediatric Surgery, Chris Hani Baragwanath Hospital, Diepkloof, Soweto, Gauteng, South Africa
,
Chris Westgarth-Taylor
1   Department of Paediatric Surgery, Chris Hani Baragwanath Hospital, Diepkloof, Soweto, Gauteng, South Africa
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Abstract

We present a case and discuss the management of a posterior cloacal variant not as yet described in the literature. A 5-week-old infant presented to our institution with a posterior cloacal variant and transposition of the clitoris and labia. After initial radiological investigations, staged operative intervention was performed over a 1-year period. This included an initial laparotomy (with drainage of hydrocolpos and formation of a colostomy), a left ureteric reimplantation and a posterior sagittal anorectoplasty due to a rectoperineal fistula. The child is under continued long-term follow-up by our specialist pediatric surgical team.

Keywords

posterior cloacal variant - anorectal malformation - cloaca


Publication History

Received: 12 November 2020

Accepted: 06 March 2021

Article published online:
18 May 2021

© 2021. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution License, permitting unrestricted use, distribution, and reproduction so long as the original work is properly cited. (https://creativecommons.org/licenses/by/4.0/)

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