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CC BY 4.0 · European J Pediatr Surg Rep. 2022; 10(01): e63-e67
DOI: 10.1055/s-0041-1741508
Case Report

Clinical Quiz—Newborn Female with an Anorectal Malformation and a Gynecological Abnormality

Anisha Apte
1   Department of General Surgery, The George Washington University School of Medicine and Health Sciences, Washington, District of Columbia, United States
,
Allison Mayhew
2   Department of Pediatric and Adolescent Gynecology, Children's National Medical Center, Washington, District of Columbia, United States
,
Elise McKenna 
3   Department of General and Thoracic Surgery, Children's National Medical Center, Washington, District of Columbia, United States
,
Veronica Gomez-Lobo
2   Department of Pediatric and Adolescent Gynecology, Children's National Medical Center, Washington, District of Columbia, United States
4   Eunice Kennedy Shriver National Institute of Child Health and Human Development, National Institutes of Health, Bethesda, Maryland, United States
,
Marc A. Levitt
3   Department of General and Thoracic Surgery, Children's National Medical Center, Washington, District of Columbia, United States
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Abstract

We present a case of a newborn female with imperforate anus who on exam was found to have a rectal fistula in the vestibule, no vaginal opening, and a normal urethra. A diagnostic laparoscopy was performed to elucidate the internal anatomy. The case is presented with a focus on surgical strategies in approaching the female patient with anorectal malformation and a Mullerian anomaly, with questions for the readers posed in a quiz format.

Keywords

anorectal malformation - imperforate anus - Mullerian anomalies - vestibular fistula - vaginal atresia


Publication History

Received: 21 March 2021

Accepted: 05 June 2021

Article published online:
13 April 2022

© 2022. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution License, permitting unrestricted use, distribution, and reproduction so long as the original work is properly cited. (https://creativecommons.org/licenses/by/4.0/)

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