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CC BY-NC-ND 4.0 · Sleep Sci 2023; 16(03): e375-e380
DOI: 10.1055/s-0043-1772817
Case Report

Obstructive Sleep Apnea Treatment with Oral Appliance in a Myotonic Dystrophy Type I Subject: A Case Report

Maria de Lourdes Rabelo Guimarães
1   Universidade Federal de Minas Gerais, Centro de Tecnologia em Medicina Molecular, Belo Horizonte, Minas Gerais, Brazil.
,
Milena Carvalho Tourino Ribeiro
2   Centro Universitário de Belo Horizonte, Faculty of Dentistry, Belo Horizonte, Minas Gerais, Brazil.
,
Thiago Antunes da Silva Barbosa
2   Centro Universitário de Belo Horizonte, Faculty of Dentistry, Belo Horizonte, Minas Gerais, Brazil.
,
Laila Gabriela de Figueiredo Costa 
3   Newton Paiva, Faculty of Dentistry, Belo Horizonte, Minas Gerais, Brazil.
,
Patricia Souza Bastos
4   Rede Sarah de Hospitais de Reabilitação, Setor de Eletrodiagnósticos, Belo Horizonte, Minas Gerais, Brazil.
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Abstract

Objective to report a myotonic dystrophy type 1 (MD1) subject with obstructive sleep apnea syndrome treated with oral appliance.

Methods A review of individual's history and records, associated with a photographic register of all diagnostic methods and literature research about the topic were done.

Final Statements This case depicts the therapeutical choices disposable to treat subjects with obstructive sleep apnea and DM1. Although considered an uncommon treatment, the oral appliances, if well indicated in adequately selected cases, can satisfactorily improve respiratory parameters, symptoms and quality of life.

Keywords

myotonic dystrophy type 1 - sleep apnea syndromes - sleepiness - oral appliance - biomarker - therapeutics


Publication History

Received: 18 October 2021

Accepted: 05 December 2022

Article published online:
11 September 2023

© 2023. Brazilian Sleep Association. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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