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Endoscopy 2003; 35(6): 531-533
DOI: 10.1055/s-2003-39659
Case Report
© Georg Thieme Verlag Stuttgart · New York

Hemobilia in Hereditary Hemorrhagic Telangiectasia: An Unusual Complication of Endoscopic Retrograde Cholangiopancreatography

T.  Costa Macedo 1 , R.  Maldonado 1 , A.  Valente 1 , R.  Palma 1 , M.  Raimundo 1 , M.  Liberato 2 , I.  Távora 3 , P.  Alexandrino 1 , M.  Carneiro de Moura 1
  • 1 Gastrenterology and Hepatology Intensive Care Unit, Dept. of Medicine II, Santa Maria Hospital, Lisbon, Portugal
  • 2 CUF Hospital, Lisbon, Portugal
  • 3 Dept. of Imaging, Santa Maria Hospital, Lisbon, Portugal
Further Information

Publication History

Submitted 22 Januar 2002

Accepted after Revision 11 November 2002

Publication Date:
03 June 2003 (online)

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Hepatobiliary manifestations of hereditary hemorrhagic telangiectasia (HHT) are rare, but often involve cholestasis. We report here a case of HHT associated with cholestasis due to common bile duct stenosis. Attempted balloon dilation of the stenosis during endoscopic retrograde cholangiopancreatography (ERCP) resulted in hemobilia. Hemostasis was achieved by adjusting the nasobiliary drain. The aim of this report is to highlight the biliary manifestations of HHT and draw attention to an unusual complication of ERCP in this setting.

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T. Costa Macedo, M.D.

UCIGE-H Hospital de Santa Maria

Av. Prof. Egas Moniz · 1649-035 Lisbon · Portugal

Fax: + 351-21-7932605

Email: tcostamacedo@clix.pt