Eur J Pediatr Surg 2003; 13(6): 421-424
DOI: 10.1055/s-2003-44736
Case Report

Georg Thieme Verlag Stuttart, New York · Masson Editeur Paris

Inflammatory Myofibroblastic Tumour of the Extrahepatic Bile Ducts: An Unusual Cause of Obstructive Jaundice in Children

İ. Büyükyavuz 1 , İ. Karnak 1 , M. Haliloglu 2 , M. E. Şenocak 1
  • 1Department of Paediatric Surgery, Hacettepe University Faculty of Medicine, Ankara, Turkey
  • 2Department of Radiology, Hacettepe University Faculty of Medicine, Ankara, Turkey
Further Information

Publication History

Received: February 5, 2003

Accepted after Revision: April 24, 2003

Publication Date:
26 January 2004 (online)

Abstract

Inflammatory myofibroblastic tumour is a rare entity in children with few reported series. The extrahepatic bile duct is an unusual location for this tumour. The authors report here the case of an 8-year-old girl presenting with obstructive jaundice due to inflammatory myofibroblastic tumour of the extrahepatic bile ducts with differential diagnosis of obstructive jaundice in children.

Résumé

Une tumeur inflammatoire myofibroblastique est rare chez les enfants. Peu de cas sont rapportés dans la littérature. Les voies biliaires extrahépatiques constituent la localisation préférentielle. Nous décrivons le cas d'une fillette de huit ans présentant un ictère par obstruction en raison d'une tumeur inflammatoire myofibroblastique au niveau des voies biliaires extrahépatiques et discutons des diagnostics différentiels de l'ictère par obstruction chez les enfants.

Resumen

El tumor miofibroblástico inflamatorio es una entidad rara en niños de la que se han publicado pocos casos. Las vías biliares extrahepáticas son una localización muy rara del tumor. Los autores presentan el caso de una niña de 8 años que sufrió ictericia obstructiva debida a un tumor miofibroblástico inflamatorio de las vías biliares extrahepáticas y discuten el diagnóstico diferencial de la ictericia obstructiva en niños.

Zusammenfassung

Ein entzündlicher myofibroblastischer Tumor ist im Kindesalter sehr selten und ungewöhnlich. Noch ungewöhnlicher ist der Ausgangspunkt im Bereich der extrahepatischen Gallenwege. In der vorliegenden Arbeit wird ein 8-jähriges Mädchen vorgestellt, das mit einer obstruktiven Gelbsucht aufgrund eines inflammatorischen myofibroblastischen Tumors der ableitenden Gallenwege erkrankte. Die Differenzialdiagnose und Therapie werden diskutiert.

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Associate Professor of Paediatric Surgery, M.D. İbrahim Karnak

Hacettepe University Faculty of Medicine

Yenişehir

06100 Ankara

Turkey

Email: ikarnak@hacettepe.edu.tr