Transient Auditory Neuropathy with Resurgence of Electrophysiological Waveforms Observed between the Neonatal Period and Age 3 Years

Abstract

Auditory neuropathy spectrum disorder (ANSD) is a spectrum of conditions marked by diminished auditory function and believed to be caused by the impaired neural transmission of auditory stimulation in the setting of functional outer hair cells. There are reports of “spontaneously resolving” or “transient” ANSD (transient auditory neuropathy [TAN]) in the literature. In this case report of TAN, we demonstrate the resurgence of the auditory brainstem response waveform morphology over a 3-year period to reveal electrophysiological testing consistent with the patient's functional hearing level by age 3 years.

Keywords

auditory neuropathy - universal newborn hearing screen - spontaneous recovery - waveforms - auditory brainstem response testing

Previous Presentation

The findings herein were presented in poster format at the Society for Ear, Nose and Throat Advances in Children (SENTAC) 44^th annual meeting in Phoenix, AZ, December 2–4, 2021.

Authors' Contributions

M. E. B.: Project conception, data acquisition, drafting work, final approval, accountability.

H. E. K.: Project conception, data acquisition, drafting work, final approval, accountability.

A. K. E.: Project conception, institutional review board process, draft revisions, final approval, accountability, all correspondence, uploading of files, approvals, submissions.

A. G.: Project conception, draft revisions, final approval, accountability.

Publikationsverlauf

Eingereicht: 29. März 2022

Angenommen: 20. Dezember 2022

Accepted Manuscript online:
08. Dezember 2023

Artikel online veröffentlicht:
23. September 2024

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