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DOI: 10.1055/s-0029-1215601
© Georg Thieme Verlag KG Stuttgart · New York
Central Hepatectomy for Hepatic Mesenchymal Hamartoma in Children
Publikationsverlauf
Publikationsdatum:
15. Mai 2009 (online)

Introduction
Hepatic mesenchymal hamartoma (HMH) is the second commonest benign hepatic tumor in children after hemangioma. Typically, it presents as a large benign multicystic liver mass in children younger than 3 years. The natural history of HMH is poorly understood, with some cases undergoing spontaneous regression and others progressing to undifferentiated (embryonal) sarcoma. Most tumors are centrally located in the liver and gradually increase in size, often reaching enormous proportions, making surgical resection challenging and leading some surgeons to advocate a non-radical resection or marsupialization of large centrally located tumors as acceptable management. In the light of recent cytogenetic studies suggesting that HMH may be a neoplasm rather than a hamartoma, complete surgical excision remains the treatment of choice. We report on a parenchyma-sparing resection technique for a centrally located HMH.
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Correspondence
Dr. W. Faraj
Institute of Liver studies
King's College Hospital
Denmark hill
London
United Kingdom
SE5 9RS
Telefon: +44/203/299 37 72
Fax: +44/203/299 35 75
eMail: wfaraj@hotmail.com