Undescended Testis Accompanying Congenital Spigelian Hernia: Is It a Reason, a Result, or a New Syndrome?

Abstract

Introduction Frequent reporting of cases of the coexistence of a Spigelian hernia (SH) with an undescended testis (UT) suggests that this phenomenon may be a syndrome. In this article, four pediatric cases in which an UT accompanies a congenital SH have been discussed in light of the literature.

Methods In this study, four cases aged between 6 months and 5 years who had a SH accompanied by an UT were evaluated and underwent surgery.

Result The patient's ages were 6 months, 1 year, 2 years, and 5 years old. The testis was observed in the opened hernia sac. The patients did not have a gubernaculum or an inguinal canal on the side of the hernia.

Conclusions Neither the theories suggesting that SH leads to an UT nor those suggesting that an UT leads to a SH are satisfactory. We believe that this coexistence may be the congenital Spigelian-cryptorchidism syndrome seen in boys. As in the four cases presented here, elements of this syndrome are defects in the Spigelian fascia and the hernia sac enveloping the testis and an absence of the gubernaculum and the inguinal canal.

Keywords

Spigelian hernia - undescended testis - syndrome

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