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Klinische Neurophysiologie 2013; 44(03): 213-218
DOI: 10.1055/s-0033-1343301
Der besondere Fall
© Georg Thieme Verlag KG Stuttgart · New York

Rasch progrediente Demenz: Enzephalitis oder Enzephalopathie?

Rapidly Progressive Dementia: Inflammation or Degeneration?
G. Ellrichmann
1   Department of Neurology, St. Josef Hospital, Ruhr-University Bochum
,
C. Lukas
2   Department of Radiology, St. Josef Hospital, Ruhr-University Bochum
,
W. J. Schulz-Schaeffer
3   National Reference Centre for Transmissible Spongiform Encephalopathies, Department of Neuropathology, University Medical Center Goettingen, Germany
,
C. Börnke
1   Department of Neurology, St. Josef Hospital, Ruhr-University Bochum
› Author Affiliations
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Publication History

Publication Date:
16 July 2013 (online)

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Warum dieser Fall?

Unser Fall zeigt, dass eine genaue Einordnung der Genese einer rasch progredienten Demenz trotz vermeintlich typischer klinischer Symptome und ausführlicher diagnostischer Maßnahmen (Bildgebung, EEG, Labor- und Liquoranalysen) oft erst durch eine Hirnbiopsie oder die Hirnsektion möglich ist. Die Therapie sollte bis zur Sicherung der Diagnose mögliche Differenzialdiagnosen berücksichtigen.

 

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