Review on Current Management and Outcome Data of Echogenic Lung Lesions and Hydrothorax of the Fetus

Abstract

This review focuses on the prenatal management and outcome of echogenic lung lesions and isolated hydrothorax of the fetus. We give an overview of the most common forms of echogenic lung lesions like cystic adenomatoid malformation of the lung and bronchopulmonary sequestration as well as of congenital high airway obstruction sequence. We review the occurrence, appearance, pathophysiology and natural history of these lesions. Furthermore we discuss selection criteria for intrauterine treatment and algorithms for prenatal surveillance of affected fetuses.

Zusammenfassung

Die Arbeit bietet eine Übersicht über das pränatale Management und aktuelle Outcomedaten von Feten mit echogenen Lungenläsionen und Feten mit Hydrothorax. Wir berichten über die häufigsten Formen echogener Lungenläsionen (cystisch adenomatoide Lungenmalformation, bronchopulmonale Sequestration sowie die Congenital High Airway Obstruction Sequence) und geben einen Überblick über Auftreten, pränatale Diagnose und die Pathophysiologie der Malformation. Außerdem diskutieren wir Selektionskriterien für eine pränatale Therapie und stellen Behandlungspfade für die intrauterine Überwachung betroffener Feten vor.

Key words

echogenic lung lesions - hydrothorax - congenital high airway obstruction sequence - cystic adenomatoid ­malformation - bronchopulmonary ­sequestration

Schlüsselwörter

echogene Lungenläsionen - Hydrothorax - congenital high airway obstruction sequence - cystisch adenomatoide Lungenmalformation - bronchopulmonale ­Sequestration

• References

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